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Pierre-Antoine Soret1, Olivier Chazouillères1, Christophe Corpechot1

  • 1Service d'hépatologie, centre de référence des maladies inflammatoires des voies biliaires et des hépatites auto-immunes (MIVB-H), centre de référence européen des maladies rares du foie (Rare-Liver), hôpital Saint-Antoine, AP-HP, Paris, France Sorbonne Université, INSERM, centre de recherche Saint-Antoine (CRSA), Paris, France.

La Revue du praticien
|January 23, 2026
PubMed
概括

低脂相关胆固醇症候群 (LPAC) 是一种罕见的遗传疾病. 诊断包括肝脏超声波,治疗通常包括ursodeoxycholic酸 (UDCA).

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