马凡综合症-综合牙科/外科管理:临床病例报告
Juan Pachano Valdiviezo1, Andrea Coello Hidalgo1, Maria Rodriguez Tates1
1Department of Odontopediatric, Carrera de Odontología, Facultad de Odontología, Universidad de Las Américas (UDLA), Quito, Pichincha, Ecuador.
International journal of clinical pediatric dentistry
|February 2, 2026
概括
本案例报告详细介绍了一名患有马凡综合征 (MFS) 和高牙症的儿童的微创治疗方法. 早期的骨科干预有助于MFS患者的永久牙喷发有牙异常.
科学领域:
- 牙科 牙科是指牙科的专业.
- 遗传学 是一个遗传学.
- 儿科 儿科 儿科
背景情况:
- 马凡综合征 (MFS) 是一种遗传性结合组织疾病,影响多个身体系统,包括口腔结构.
- 在MFS的口腔表现可以包括超,一种涉及额外牙的情况,影响部发育和喷发模式.
- 诊断MFS依赖于临床和遗传标准 (根特标准),牙异常需要专门注意.
研究的目的:
- 描述患有马凡综合征 (MFS) 的儿科患者的超的最小侵入性和预防性治疗方法.
- 突出早期牙科和骨科干预对患有牙科并发症的MFS患者的重要性.
- 介绍一个案例研究,说明MFS的综合牙科/外科管理策略.
主要方法:
- 评估了一名怀疑MFS和上牙异常的6岁男性患者.
- 临床检查,周周放射和断层扫描检查被用来诊断影响中央切口突发的高.
- 制定了一项治疗计划,包括微创手术和预防性骨科扩张.
主要成果:
- 诊断证实了绝对中心切口部的超,扰乱了正常的喷发时间表.
- 一种微创手术方法被成功规划和执行.
- 开始了预防性骨科治疗,以便为永久牙喷发提供足够的空间.
结论:
- 马方综合征呈现出严重的牙科并发症,需要仔细考虑和管理.
- 早期诊断和跨学科治疗对于优化儿科MFS患者的治疗结果至关重要.
- 最少侵入性的手术和骨科干预可以有效地解决MFS中的牙异常,促进正确的牙喷发.
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