成年后晚期诊断的双边先天性门缩症:一个病例报告
Fares Abboud1, Sultaneh Haddad2, Ghadeer Ibrahim3
1Damascus University, Faculty of Medicine, Fayez Mansour St, Mazzeh, PO Box 30621, Damascus, Syria.
Journal of surgical case reports
|February 23, 2026
概括
kongenital choanal atresia是一种罕见的鼻腔阻塞,可以影响成年人. 本案例研究详细介绍了38岁女性长期症状的内镜修复成功的情况.
科学领域:
- 耳鼻喉科 耳鼻喉科 耳鼻喉科
- 遗传性疾病 遗传性疾病
背景情况:
- 门缩症是一种先天性鼻腔阻塞,通常在新生儿中诊断出来.
- 成人呈现,特别是双边呈现,很少见,并且经常被误诊.
- 延迟诊断可能导致慢性鼻腔和耳部症状.
研究的目的:
- 报告一个罕见的成人发病双边道缩症的病例.
- 要突出诊断挑战和成年人的临床表现.
- 为了证明内镜外科修复的有效性.
主要方法:
- 评估了一名38岁的女性,她有20年的鼻腔和耳部症状史.
- 诊断工具包括CT成像,内镜和鼻胃管探测.
- 手术干预包括动脉板的内镜切除和带支架的上肠.
主要成果:
- 证实了完全的双边小门阻塞.
- 内镜修复导致了成功的门通透.
- 患者经历了症状的缓解,并在手术后四个月内保持了通透性.
结论:
- 在患有慢性鼻腔阻塞的成年人中,应考虑先天性门缩.
- 内镜手术是一种有效的治疗成人门缩症.
- 早期诊断和干预可以预防长期并发症.
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