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Updated: Feb 27, 2026

Implementation of Non-invasive Point of Care Transient Elastography for Evaluation of Liver Disease in Pediatric Populations with Cystic Fibrosis
05:56

Implementation of Non-invasive Point of Care Transient Elastography for Evaluation of Liver Disease in Pediatric Populations with Cystic Fibrosis

Published on: August 29, 2025

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超越BMI:CFTR调节器在囊性纤维化中的营养恢复和功能影响

Giovanna Linguiti1, Vanja Granberg1, Giuseppina Leonetti1

  • 1Pediatric Unit "B. Trambusti", Cystic Fibrosis Regional Reference Center, Department of Interdisciplinary Medicine, University of Bari "Aldo Moro", 70124 Bari, Italy.

Biology
|February 26, 2026
PubMed
概括

在囊性纤维化患者中,CFTR调节器显著改善BMI和肺功能 (FEV1). 虽然有益,但它们也增加了超重和肥胖的风险,需要专注于代谢健康而不仅仅是体重增加.

关键词:
身体构成 身体组成身体质量指数 (BMI) 是指身体质量指数.囊性纤维化症是什么选择一个接收器/接收器/接收器或接收器.伊瓦卡夫托尔 (Ivacaftor) 是一个营养 营养 营养 营养肥胖症 肥胖症 肥胖症 肥胖症

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