马瓦卡门治疗对心肌缩功能的影响,通过3D心声学评估

Roberto Polizzi1, Grazia Canciello1, Leopoldo Ordine1

  • 1Department of Advanced Biomedical Sciences, University Federico II of Naples, Naples, Italy.

JACC. Case reports
|March 4, 2026
PubMed
概括

对于阻塞性多变性心肌病 (oHCM) 的Mavacamten治疗改善了症状并减少了阻塞. 心声图显示区域性变化,而不是全球性功能障碍,这表明有针对性的治疗有好处.

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