一个孩子的孤立异常左上肺静脉连接:一个病例报告
Alwaleed Al-Dairy1, Basheer AlRefai2, Bassam Khrma2
1Damascus University, Damascus, Syrian Arab Republic.
International journal of surgery case reports
|March 12, 2026
概括
手术修复左侧部分异常肺静脉连接 (PAPVC) 有效地解决了症状,并预防了右心力衰竭. 这种罕见的先天性心脏缺陷需要及时干预,以获得最佳的长期结果.
科学领域:
- 心脏病学 心脏病学
- 遗传性心脏病是一种先天性心脏病.
- 胸部外科手术 胸部外科手术
背景情况:
- 部分异常肺静脉连接 (PAPVC) 是一种罕见的先天性心脏缺陷.
- 左侧PAPVC,涉及左上肺静脉,不常见,往往是晚诊断.
- 右心体积过载可能导致呼吸不全和复发性呼吸道感染.
研究的目的:
- 提出一个孤立的左侧PAPVC病例,成功进行手术修复.
- 突出早期诊断和干预症状PAPVC的重要性.
- 强调非侵入性成像在诊断PAPVC中的作用.
主要方法:
- 使用非侵入性成像 (TTE/CTA) 的诊断.
- 手术修复涉及心肺旁路术下的左心房异常肺静脉对心肺静脉进行解剖.
- 肺静脉排水和临床状态的术后评估.
主要成果:
- 成功的手术纠正孤立的左上肺静脉排水.
- 呼吸不全和呼吸道症状在1年的随访后消失.
- 肺静脉排水正常化,手术后没有右心扩张.
结论:
- 对症状性PAPVC的早期手术干预对于预防不可逆转的心脏并发症至关重要.
- 准确的非侵入性成像对于诊断和手术规划至关重要.
- 精细的外科手术技术确保了PAPVC修复的良好长期结果.
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