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[Cacchi Ricci disease. Report of a case]
P Fernández García1, S F Marco Doménech, R M Piqueras Olmeda
1Servicio de Radiodiagnóstico, Hospital General de Castellón, Castellón de la Plana, España.
Objective:
To present a case of medullary sponge kidney (Cacchi-Ricci disease) with special reference to the radiologid findings that permit early diagnosis of this rare condition.
Methods:
The most relevant clinical features and radiological findings in a patient with Cacchi-Ricci disease are described.
Results/Conclusions:
Medullaty sponge kidney, tubular ectasia or Cacchi-Ricci disease is a congenital renal medullary cystic disease that is asymptomatic in most of the cases, but can also present with hematuria, urinary infection or renal colic, with the characteristic spony, porous appearance of the dilated collecting tubules and small calculi in the papilla or renal pyramids on the IVP and, if numerous, also on US. This condition should be distinguished from nephrocalcinosis.