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Tongue reduction in Beckwith-Weidemann syndrome
A Kacker1, C Honrado, D Martin
1Lenox Hill Hospital and Manhattan Eye, Ear and Throat Hospital, 2nd Floor, 186 East 76th Street, New York, NY 10021, USA.
Objective:
To review our experience with patients with macroglossia as a component of Beckwith-Weidemann Syndrome (BWS).
Design:
Chart review of six patients treated with BWS.
Setting:
Tertiary care teaching hospital.
Patients:
Six patients diagnosed with BWS and macroglossia.
Interventions:
Four patients underwent at least one surgical procedure to address their macroglossia. The surgical options and potential complications are discussed.
Results:
Three patients who have undergone tongue reduction have a functioning tongue with normal mobility. Two patients have required tracheotomy as apart of their management and still have significant tongue enlargement.
Conclusions:
Macroglossia as a part of BWS may present a difficult management problem. Various methods of tongue reductions have been reported with mixed results.