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Bilateral ethmoidal mucocele in cystic fibrosis: report of a case

D C Thomé1, R L Voegels, R A Cataldo de la Cortina

  • 1Department of Otolaryngology of the University of São Paulo Medical School, Alameda Itú 483 apto 172, 01421-000, São Paulo, Brazil. dthome@dialdata.com.br

International Journal of Pediatric Otorhinolaryngology
|September 28, 2000
PubMed

Insights

This study details a rare case of bilateral ethmoidal mucoceles in a 10-month-old infant with cystic fibrosis, a condition previously unreported in such young patients. The findings highlight early sinonasal complications in pediatric cystic fibrosis.

Area of Science:

  • Otolaryngology
  • Pediatrics
  • Genetics

Background:

  • Cystic Fibrosis (CF) is a genetic disorder affecting multiple organs, including the sinonasal tract.
  • Sinonasal disease is a common complication in CF patients, often leading to mucoceles.
  • Previous literature reports on pediatric CF patients with sinonasal mucoceles are scarce.

Observation:

  • A 10-month-old male infant presented with bilateral ethmoidal mucoceles.
  • This presentation is unique due to the patient's young age and bilateral involvement.
  • The patient was diagnosed with cystic fibrosis.

Findings:

  • This case represents the youngest pediatric patient reported with bilateral ethmoidal mucoceles associated with cystic fibrosis.
  • The patient's presentation differs from previously reported cases, which involved older children and unilateral mucoceles.
  • This highlights the potential for early and bilateral sinonasal complications in CF.

Implications:

  • Early recognition of sinonasal mucoceles in infants with CF is crucial for timely intervention.
  • This case expands the understanding of sinonasal manifestations in pediatric cystic fibrosis.
  • Further research is warranted to explore the trajectory of sinonasal disease in very young CF patients.

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