Adult aortic arch atresia
1Department of Cardiovascular Surgery, Daini Okamoto General Hospital, Kyoto, Japan.
The Japanese Journal of Thoracic and Cardiovascular Surgery : Official Publication of the Japanese Association for Thoracic Surgery = Nihon Kyobu Geka Gakkai Zasshi
|October 13, 2000
Summary
A rare congenital heart defect, aortic arch atresia, was successfully treated in a 29-year-old woman using prosthetic aortic arch reconstruction. This surgical intervention allowed for a positive long-term outcome, demonstrating the efficacy of corrective procedures.
Area of Science:
- Cardiovascular Surgery
- Congenital Heart Defects
- Pediatric Cardiology
Background:
- Aortic arch atresia is a severe congenital cardiovascular anomaly with limited survival to adulthood without surgical intervention.
- Celoria-Patton Type A atresia represents a specific subtype of this rare condition.
- Adult survival with untreated aortic arch atresia is exceptionally uncommon.
Observation:
- A 29-year-old woman presented with Celoria-Patton Type A aortic arch atresia.
- The patient had no intracardiac shunt.
- This case highlights adult presentation of a typically pediatric condition.
Findings:
- Primary surgical correction was performed, involving aortic arch reconstruction with prosthetic interposition.
- The persistent ductus arteriosus was divided.
- The patient experienced an uneventful postoperative recovery.
Implications:
- This successful surgical correction demonstrates the feasibility of treating adult aortic arch atresia.
- The findings suggest improved long-term outcomes are possible with timely intervention.
- This case expands the understanding of surgical management for rare congenital cardiovascular anomalies in adults.
Related Concept Videos
01:14The Aorta
The aorta is the largest artery in the human body. It originates from the left ventricle of the heart and extends down to the abdomen, where it splits into two smaller arteries. Structurally, it can be divided into four main parts: the ascending aorta, the aortic arch, the thoracic aorta, and the abdominal aorta.
The average diameter of the aorta is approximately 2-3 cm, but the size can vary depending on the section of the aorta and the individual's age, sex, and body size. The aorta is...
The average diameter of the aorta is approximately 2-3 cm, but the size can vary depending on the section of the aorta and the individual's age, sex, and body size. The aorta is...
01:10The Arch of Aorta
The coronary arteries, originating from the ascending aorta, bifurcate from two sinuses located within the ascending aorta. Positioned just above the aortic semilunar valve, these sinuses house essential aortic baroreceptors and chemoreceptors, crucial for maintaining cardiac function. The left coronary artery and the right coronary artery branch off from the left posterior and anterior aortic sinuses, respectively.
Encircling the heart, the coronary arteries form a ring-like structure before...
Encircling the heart, the coronary arteries form a ring-like structure before...
01:15Thoracic Aorta
The thoracic section of the aorta begins at the T5 vertebra and extends to the T12 level at the diaphragm, initially progressing through the mediastinum to the left of the spinal column. Throughout its course in the thoracic segment, the thoracic aorta emits various offshoots known collectively as visceral and parietal branches. The branches that predominantly supply blood to visceral organs are termed visceral branches and include bronchial, pericardial, esophageal, and mediastinal arteries,...
01:22Aortic Regurgitation II: Clinical Features and Diagnostic Tests
Aortic valve regurgitation (AR) occurs when the aortic valve fails to close properly, allowing blood to flow backward from the aorta into the left ventricle. This backflow can result in two distinct clinical presentations: acute and chronic AR, each characterized by its own set of symptoms and physical findings.Acute Aortic RegurgitationAcute AR presents with a sudden onset of severe symptoms. Patients typically experience profound dyspnea (shortness of breath), chest pain, and signs of left...
01:30Aneurysm I: Introduction
An aortic aneurysm is a localized outpouching or dilation at a weak point in the artery wall. It may involve different parts of the aorta, such as the abdominal aorta, aortic arch, or thoracic aorta.Etiological factorsSeveral disorders are associated with aortic aneurysms.Congenital causes, such as primary connective tissue disorders like Marfan syndrome, impact the integrity and strength of connective tissues, notably affecting the aorta. Marfan syndrome is a genetic disorder that specifically...
01:21Aneurysm II: Clinical Manifestations and Diagnostic Studies
Thoracic, aortic arch and abdominal aneurysms are significant vascular conditions that can present with various clinical manifestations and lead to serious complications. Understanding these manifestations and the appropriate diagnostic studies is essential for effective management and treatment.Thoracic Aortic AneurysmsThoracic aortic aneurysms often remain asymptomatic until they reach a size that impinges on adjacent structures. They typically cause deep, diffuse chest pain that radiates to...