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Definite improvement in left ventricular function at six years after the Takeuchi procedure.
1Department of Pediatric Cardiovascular Surgery, Heart Institute of Japan, Tokyo Women's Medical University, 8-1 Kawadacho, Shinjuku-ku, Tokyo 162-8666, Japan.
Summary
A six-year-old girl with anomalous left coronary artery from the pulmonary artery showed improved heart function after the Takeuchi procedure. The intrapulmonary tunnel remained patent, and surgically induced stenosis was successfully treated.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Surgical Reconstruction
Background:
- Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital heart defect.
- Early diagnosis and surgical correction are crucial for improving left ventricular function and long-term outcomes.
Observation:
- A 6-year-old female patient underwent the Takeuchi procedure for ALCAPA at 4 months of age.
- Pre-operative assessment revealed severely deteriorated left ventricular function.
- Follow-up at 6 years post-procedure showed significant improvement in cardiac function and resolution of mitral regurgitation.
Findings:
- The intrapulmonary tunnel created during the Takeuchi procedure remained patent, ensuring adequate blood supply to the anomalous left coronary artery.
- Supravalvular stenosis developed due to shrinkage and thickening of the equine pericardium used for pulmonary artery reconstruction.
- The stenosis was successfully managed with autologous pericardial patch angioplasty.
Implications:
- The Takeuchi procedure can lead to favorable long-term outcomes in ALCAPA patients, including improved ventricular function.
- Monitoring for and timely intervention for potential complications like graft stenosis are essential.
- Autologous pericardium is a viable option for managing graft-related stenosis in complex pediatric cardiac surgeries.