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[Subacute sclerosing panencephalitis]
1Unidade de Neurologia, Hospital de Dona Estefânia, Lisboa.
Acta Medica Portuguesa
|January 13, 2001
Abstract:
Subacute sclerosing panencephalitis is a slowly progressive neurodegenerative disorder occurring in childhood and adolescence and is characterised by dementia, ataxia, myoclonias and other neurological focal signs, with an invariably fatal outcome. The author reviews the subject, focussing on epidemiology, clinical features, measles virus behaviour, host immune reactions, measles prophylaxis and treatment proposals.