Vascular hamartoma of the orbit

The aim of this presentation is to report a combined form of vascular malformation of the orbit. A 2-year-old girl had a four-month history of severe proptosis in the right eye. The patient had intermittent proptosis in association with a common cold. The globe was displaced downward and extraocular motility was markedly limited. Multiple intraconal and some extraconal cysts were removed with transcutaneous transseptal anterior orbitotomy. Histological examination showed several characteristics of vascular anomaly. There were malformatively dilated veins intermingled with dilated lymphatic channels, focal cavernous and capillary hemangiomatous features. This combined form of vascular anomaly can be presented as a venous lymphatic malformation associated with hemangiomatous features.