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[Cystic fibrosis: nutritional considerations].
M Molina Arias1, G Prieto Bozano, J Sarría Osés
1Servicio de Gastroenterología y Nutrición. Hospital Infantil Universitario La Paz. Madrid. molinaarias@worldonline.es
Anales Espanoles De Pediatria
|June 20, 2001
Summary
Improved nutrition and treatment have enhanced survival for cystic fibrosis patients. Nutritional support is crucial, as malnutrition worsens respiratory function and disease outcomes.
Area of Science:
- Medical Science
- Nutritional Science
- Pulmonology
Context:
- Cystic Fibrosis (CF) patients experience increased survival due to advancements in treatment and nutritional support.
- Malnutrition is a common complication in CF, affecting 20% of patients and linked to poorer disease prognosis.
- Negative energy-protein balance in CF arises from increased energy expenditure, elevated nutritional needs, and reduced oral intake.
Purpose:
- To highlight the critical role of nutritional status in Cystic Fibrosis management.
- To emphasize the need for regular monitoring of clinical, anthropometrical, and functional nutritional parameters in CF patients.
- To outline essential dietary recommendations and supplementation strategies for individuals with CF.
Summary:
- Malnutrition significantly impacts respiratory function and overall outcomes in Cystic Fibrosis.
- Effective management requires ensuring nutritional intake exceeds requirements, with specific support when necessary.
- A hypercaloric, hyperproteotic diet with adequate fats, normal carbohydrates, and pancreatic/vitamin supplements (if needed) is recommended for CF patients.
Impact:
- Optimized nutritional support can improve respiratory function and quality of life for CF patients.
- Proactive nutritional interventions are key to mitigating disease progression and improving survival rates in Cystic Fibrosis.
- This approach underscores the importance of a multidisciplinary strategy involving nutritionists and healthcare providers in CF care.