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Isolated congenital left ventricular diverticulum in adults
D Vaidiyanathan1, D Prabhakar, K Selvam
1Department of Cardiology, Madras Medical College, Chennai. prabhud@vsnl.com
Indian Heart Journal
|June 29, 2001
Summary
Congenital left ventricular diverticulum is a rare cardiac anomaly with varied presentations. Early diagnosis requires a high index of suspicion during imaging like chest X-rays and echocardiography.
Area of Science:
- Cardiology
- Congenital Heart Disease
Background:
- Isolated congenital ventricular diverticulum is a rare condition, typically originating from the left ventricle.
- Its clinical presentation is highly variable, making diagnosis challenging.
Observation:
- Three cases of isolated congenital left ventricular diverticula in patients aged 17-30 years are presented.
- Chest X-ray initially suggested a cardiac anomaly, with echocardiography and angiocardiography confirming the diagnosis.
- Diverticula were located at the left ventricular apex (two cases) and base (one case).
Findings:
- Congenital left ventricular diverticulum exhibits diverse clinical presentations.
- Diagnosis relies on a high index of suspicion when interpreting chest X-rays and echocardiograms.
- Key diagnostic features include a contractile accessory chamber with a narrow neck and an electrocardiogram lacking Q waves.
Implications:
- This condition underscores the importance of thorough imaging interpretation in diagnosing rare cardiac anomalies.
- Increased awareness can lead to earlier and more accurate diagnosis of congenital left ventricular diverticulum.
- Understanding the varied presentations aids in clinical decision-making for affected individuals.