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Congenital isolated upper limb hypertrophy with hand abnormality--a report of 2 cases
1Department of Hand Surgery, Singapore General Hospital, Singapore. ghstlc@sgh.com.sg
Insights
Congenital isolated hypertrophy of the left upper limb can cause hand deformities. Surgical interventions, including muscle excision and osteotomies, successfully corrected these deformities and restored hand function in two pediatric cases.
Area of Science:
- Orthopedics
- Pediatric Surgery
- Hand Surgery
Background:
- Congenital isolated hypertrophy of the upper limb is a rare condition.
- Hand deformities can significantly impact function and quality of life.
Observation:
- Two pediatric cases presented with congenital isolated hypertrophy of the left upper limb and distinct hand deformities.
- Case 1: A 4-year-old girl with splayed fingers and abducted thumb due to anomalous muscles.
- Case 2: An 8-year-old boy with severe ulnar drift (windblown-like hand).
Findings:
- Surgical excision of anomalous muscles corrected the deformity in Case 1.
- Corrective osteotomies and ligament reconstruction resolved the ulnar drift in Case 2, with no recurrence at follow-up.
- Both patients achieved good hand function post-operatively.
Implications:
- Congenital isolated hypertrophy with hand deformities is treatable with targeted surgical approaches.
- Early diagnosis and intervention are crucial for optimal functional outcomes in pediatric patients.
- These cases highlight the effectiveness of different surgical techniques for specific hand deformities associated with limb hypertrophy.
Abstract:
Two cases of congenital isolated hypertrophy of the left upper limb with different hand deformities are described. A 4-year-old girl had splayed fingers and an abducted thumb due to anomalous muscles. Excision of these muscles corrected the deformity. The other, an 8-year-old boy, had severe ulnar drift of the fingers (windblown-like hand). He had corrective osteotomies of the second and third metarcarpals and reconstruction of the collateral ligaments. The deformity was corrected and at the latest follow up there was with no recurrence of the deviation. Both cases regained good hand function.