[Non familial juvenile multiple polyposis. A case report]
1Servicio y Departamento de Cirugía y Anatomía Patológica, Hospital Clínico San Borja Arriarán, Campus Centro, Facultad de Medicina, Universidad de Chile.
Revista Medica De Chile
|December 1, 2001
Summary
A teenage girl with severe rectal bleeding and prolapse underwent surgery for over 200 polyps. Successful proctocolectomy resulted in a complete recovery, with the patient remaining asymptomatic after 24 months.
Area of Science:
- Gastroenterology
- Colorectal Surgery
Background:
- Juvenile polyposis can present with significant gastrointestinal bleeding and prolapse.
- Early diagnosis and intervention are crucial for managing severe pediatric gastrointestinal conditions.
Observation:
- A 15-year-old female presented with severe hematochezia, anemia, hemodynamic decompensation, rectal prolapse, and spontaneous polyp expulsion.
- No family history of polyposis was reported, and investigations excluded polyps in other digestive segments.
- Colonoscopy revealed over 200 retention polyps with adenomatous areas and mild atypia from cecum to rectum.
Findings:
- The patient underwent proctocolectomy with ileal pouch and sphincteric preservation using a mechanical suture.
- Pathological analysis confirmed retention polyps with adenomatous changes and mild atypia.
Implications:
- Surgical intervention can effectively treat severe cases of juvenile polyposis with significant complications.
- Successful ileal pouch reconstruction preserves sphincter function, leading to good long-term outcomes and quality of life.
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