Related Experiment Videos
Dyke-Davidoff-Masson syndrome.
Haydar A Tasdemir1, Lutfi Incesu, Alper K Yazicioglu
119 Mayis University Medical School, Department of Pediatrics, Kurupelit, Samsun, Turkey.
Clinical Imaging
|January 30, 2002
Summary
This study examined Dyke-Davidoff-Masson syndrome (DDMS) in five patients, finding no correlation between disease duration, parenchymal changes, and calvarial alterations. Radiological assessments revealed varied findings across cases.
Area of Science:
- Neurology
- Radiology
- Medical Imaging
Background:
- Dyke-Davidoff-Masson syndrome (DDMS) is a rare congenital neurological disorder.
- Characterized by unilateral cerebral hemiatrophy and ipsilateral skull changes.
- Clinical and radiological manifestations can be highly variable.
Purpose of the Study:
- To report five cases of Dyke-Davidoff-Masson syndrome (DDMS).
- To analyze diverse clinical and radiological findings in DDMS.
- To investigate potential relationships between specific DDMS parameters.
Main Methods:
- Case series of five patients diagnosed with DDMS.
- Utilized magnetic resonance (MR) and computerized tomography (CT) imaging.
- Evaluated lesion location, midline shift, calvarial/sinus/mesencephalon changes, and contralateral hypertrophy.
Main Results:
- Observed varying degrees of all evaluated parameters across the five patients.
- Demonstrated diverse clinical presentations and radiological findings.
- No significant correlation found between parenchymal and calvarial changes.
Conclusions:
- No relationship identified between parenchymal and calvarial changes in DDMS.
- The time after disease onset did not correlate with the extent of morphologic and pathological changes.
- DDMS exhibits significant heterogeneity in its presentation and progression.