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Continuous Manual Exchange Transfusion for Patients with Sickle Cell Disease: An Efficient Method to Avoid Iron Overload
05:23

Continuous Manual Exchange Transfusion for Patients with Sickle Cell Disease: An Efficient Method to Avoid Iron Overload

Published on: March 14, 2017

Care of the child with sickle cell disease: acute complications

L D Jakubik1, M Thompson

  • 1Department of Nursing, Children's Hospital of Philadelphia, Philadelphia, PA, USA.

Pediatric Nursing
|May 25, 2002
PubMed

Insights

Sickle cell disease (SCD) management in children requires nurses to understand its genetic basis and complications. Prompt treatment and preventative measures are vital for avoiding severe outcomes and improving patient care.

Area of Science:

  • Hematology
  • Genetics
  • Pediatrics

Background:

  • Sickle cell disease (SCD) is a group of inherited blood disorders.
  • It is characterized by abnormal hemoglobin S, leading to various complications.
  • Common acute issues in children include pain episodes, fever, and spleen complications.

Purpose of the Study:

  • To highlight the critical role of staff nurses in managing pediatric SCD.
  • To emphasize the importance of understanding SCD pathophysiology for effective care.
  • To underscore the need for knowledge in genetics, pathophysiology, and management strategies.

Main Methods:

  • Review of SCD pathophysiology, including vaso-occlusion, hemolysis, and immune system involvement.
  • Discussion of common acute complications and their management.
  • Emphasis on nursing interventions and patient/family education.

Main Results:

  • Nurses play a key role in prompt treatment and prevention of adverse SCD outcomes.
  • Understanding basic science (genetics, pathophysiology) is essential for effective nursing care.
  • Knowledge of medical and nursing management, plus education materials, is crucial.

Conclusions:

  • Nurses require comprehensive knowledge of SCD to provide optimal care for affected children.
  • Effective management involves understanding the disease's genetic and pathophysiological basis.
  • Preventative measures and patient education are integral to improving clinical outcomes in pediatric SCD.

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