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Erdheim-Chester disease: a bilateral orbital mass as an indication of systemic disease
Shantha Amrith1, Cze Hong Low, Elizabeth Cheah
1Consultant Ophthalmologists, Mount Elizabeth Medical Center, Singapore
Orbit (Amsterdam, Netherlands)
|June 5, 2002
Abstract:
A case of bilateral orbital mass and xanthelasma of the eyelids is presented. Histology confirmed it to be a form of histiocytosis, possibly an Erdheim-Chester disease. This was further confirmed by the presence of a retroperitoneal mass and hydronephrosis, which resolved with treatment. A review of the literature on and pathological features of this rare fatal disease is presented.