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The Middle-East connection of Wolman Disease
Durjoy K Shome1, Emtethal Al-Jishi, John F Greally
1Department of Pathology, Salmaniya Medical Complex, PO Box 12, Manama, Bahrain. shome@batelco.com.bh
Saudi Medical Journal
|June 19, 2002
Abstract:
The clinical, laboratory and cytological features of 2 Bahraini infants with Wolman's disease are described. While one of the cases showed the classical diagnostic features, the other case exhibited a few atypical features such as lack of adrenal calcification and unusual morphology of vacuolated marrow macrophages. Literature review shows that this disorder may not be rare in this region.