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Synovial sarcoma arising from the hypopharynx: a case report
Cetin Vural1, Asli Batur Caliş, Bilge Bilgiç
1Department of Otolaryngology, Sişli Etfal Training Hospital, Istanbul, Turkey.
Summary
This case report details a rare hypopharyngeal synovial sarcoma in a young male. The tumor recurred 12 years post-surgery but was successfully treated with further surgery and radiotherapy.
Area of Science:
- Oncology
- Surgical Pathology
- Head and Neck Surgery
Background:
- Synovial sarcoma is a rare soft tissue neoplasm, accounting for a small percentage of all sarcomas.
- Head and neck region represents an uncommon site for synovial sarcoma, typically occurring in the parapharyngeal space.
- Hypopharyngeal localization of synovial sarcoma is exceptionally rare, presenting unique diagnostic and therapeutic challenges.
Observation:
- A 22-year-old male presented with a synovial sarcoma primarily located in the hypopharynx.
- Initial treatment involved wide surgical excision followed by adjuvant radiotherapy.
- A significant recurrence of the synovial sarcoma was observed at the primary site 12 years after the initial surgery.
Findings:
- The delayed recurrence highlights the potential for late relapse in synovial sarcomas, even after seemingly successful primary treatment.
- The patient achieved a disease-free status for five years following salvage treatment for the recurrent tumor.
- This case underscores the importance of long-term surveillance for patients treated for synovial sarcoma.
Implications:
- This case contributes to the limited literature on hypopharyngeal synovial sarcoma, emphasizing its rarity and potential for late recurrence.
- Findings suggest that aggressive surgical management and radiotherapy may be effective even for late recurrences.
- Long-term follow-up is crucial for early detection of recurrence in patients with head and neck synovial sarcomas.