[Maculopathy in Curschmann-Steinert myotonic dystrophy]

Besides hereditary macular dystrophies as well as acquired and age-related macular degenerations, systemic disorders should also be considered as a rare cause of maculopathy. In particular, myotonic dystrophy (Curschmann-Steinert syndrome), also characterized by the presence of ptosis and a pathognomic star-shaped cataract, should be taken into account since a reticular dystrophy of the retinal pigment epithelium could be observed, resulting in a visual impairment of various degrees. A clinical case have been retrospectively reviewed and reported in this paper.