Agenesis of the right lobe of liver

Congenital anomalies involving the lobes of the liver are rare. Hypoplasia and agenesis occur more often in the left lobe. Agenesis of the right lobe is a rare anomaly with only about 42 cases reported in literature. In this communique we report one such case of agenesis of the right lobe of liver. A brief review of literature is made and its diagnosis and differential diagnosis are discussed.