[Pathologic anatomy and morphogenesis of the "pagoda" syndrome]

A rare case of congenital intestinal obstruction of hereditary nature, the so-called "pagoda" syndrome, is described. This syndrome consists in atresia of the initial department of the jejunum, considerable shortening of the intestine and in a peculiar deformation of the remaining part of the small intestine and its mesentery. The pattern of the blood supply of the intestine and its morphology support the suggestion that this syndrome is underlayed by agensia of the anterior knee of the middle intestine of the embryo, and its teratogenetic termination period does not exceed the first four weeks of embryogenesis.