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Congenital partial pericardial defect in a neonate: a case report
Surasak Puvabanditsin1, Eugene Garrow, Anjali Biswas
1Department of Pediatrics, Jersey City Medical Center, New Jersey 07304, USA.
American Journal of Perinatology
|June 13, 2003
Summary
Congenital partial absence of the pericardium, a rare condition, was observed in a neonate with hypoplastic left heart syndrome. This rare cardiac defect led to severe heart failure and the infant
Area of Science:
- Cardiovascular Pathology
- Neonatal Medicine
- Congenital Malformations
Background:
- Congenital partial absence of the pericardium is a rare condition.
- Hypoplastic left heart syndrome (HLHS) is a severe congenital heart defect.
Observation:
- A neonate presented with severe heart failure due to a hypoplastic left ventricle.
- The infant exhibited signs of intractable congestive heart failure shortly after birth.
Findings:
- Necropsy confirmed a hypoplastic left ventricle and a transverse biventricular constriction, indicative of partial pericardial absence.
- Associated malformations included left hydronephrosis and a bicornuate uterus.
Implications:
- This case highlights a rare association between pericardial defects and complex congenital heart disease.
- Understanding these rare entities is crucial for diagnosis and management of neonatal cardiac anomalies.