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[Compressive optic neuropathy caused by fibrous dysplasia]
R Messaoud1, S Zaouali, A Ladjimi
1Service d'Ophtalmologie, Hôpital Universitaire Fattouma Bourguiba, 5019 Monastir, Tunisie.
Journal Francais D'Ophtalmologie
|August 12, 2003
Summary
Craniofacial fibrous dysplasia can cause compressive optic neuropathy, leading to vision loss. Prompt diagnosis and treatment, such as systemic steroids, can significantly improve visual function in affected patients.
Area of Science:
- Ophthalmology
- Neurology
- Genetics
Background:
- Fibrous dysplasia is a bone disorder that can affect the craniofacial region.
- Compressive optic neuropathy is a potential complication of craniofacial fibrous dysplasia, leading to visual impairment.
Observation:
- A 28-year-old woman presented with decreased vision in the left eye.
- Examination revealed reduced visual acuity, an afferent pupillary defect, and a cecocentral scotoma.
- Imaging showed craniofacial fibrous dysplasia compressing the left optic nerve.
Findings:
- Systemic steroids led to rapid visual improvement, resolution of the pupillary defect, and visual field recovery.
- Despite declining surgery, the patient remained stable during follow-up.
Implications:
- Compressive optic neuropathy is a critical consideration in patients with craniofacial fibrous dysplasia.
- Early diagnosis and management are essential for preserving or restoring visual function.