[Ankyloglossum superius: apropos of a case]

The authors report a rare observation of ankyloglossum superius i.e. the attachment of the tip of the tongue to the anterior part of the palate, with an ectrodactyl of the fingers and toes. Following a review of the literature, this provide an opportunity to recall this pathology, the physiopathogenesis of which remains unknown falling within syndromes of malformation affecting both the mouth, face and limb, namely orofacio-digital syndromes and syndromes of hypogenesis of the mouth, jaw and limbs.