Common bile duct obstruction due to pancreatic involvement in the von Hippel-Lindau syndrome

Pancreatic involvement in the von Hippel-Lindau syndrome occurs frequently, but is nearly always asymptomatic. Until now, only two cases of bile duct obstruction as a complication of this syndrome have been reported. We present another report of cholestatic jaundice in a patient with the von Hippel-Lindau syndrome and multiple pancreatic cystic lesions, treated by endoscopic implantation of a biliary stent.