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[Acute neonatal appendicitis in an inguinal hernia].
N Guelouz1, V Rigourd, M A Dommergues
1Service de réanimation néonatale, institut de puériculture et de périnatalogie, 26, boulevard Brune, 75014 Paris, France.
Summary
Neonatal appendicitis is a rare surgical emergency, particularly in premature infants. Early diagnosis and surgical intervention are crucial for improving outcomes in these critical cases.
Area of Science:
- Pediatric Surgery
- Neonatal Medicine
- Surgical Emergencies
Background:
- Neonatal appendicitis is a rare but serious condition, accounting for 0.1% of all infantile appendicitis cases.
- Premature infants are disproportionately affected, representing 50% of neonatal appendicitis cases.
- The condition presents diagnostic challenges, often requiring surgical intervention for definitive diagnosis.
Observation:
- A case report details a premature infant with occlusive syndrome, sepsis, and an inflammatory skin reaction requiring emergency laparotomy.
- Intraoperative findings revealed suppurative acute appendicitis with local peritonitis, complicated by a strangulated appendix within an inguinal hernia.
- Two primary clinical presentations exist: abdominal (mimicking necrotizing enterocolitis) and intra-hernial.
Findings:
- The abdominal presentation (two-thirds of cases) is frequently diagnosed late, leading to diffuse peritonitis and a mortality rate exceeding 50%.
- The intra-hernial presentation (one-third of cases) is often diagnosed and treated early due to characteristic inguino-scrotal induration, with a near-zero mortality rate.
- Inguinal hernias in premature infants can mask appendicitis, highlighting the importance of considering this diagnosis in cases of inguino-scrotal inflammation.
Implications:
- Prompt recognition of intra-hernial appendicitis is vital, even in the presence of common inguinal hernias in premature infants.
- Suspicion of appendicitis should be raised with any inguino-scrotal inflammation in neonates.
- Timely and urgent surgical management significantly improves the prognosis for neonatal appendicitis, reducing mortality and morbidity.