Esophageal motor function in congenital esophageal stenosis

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Hisayoshi Kawahara1, Takaharu Oue, Hiroomi Okuyama

  • 1Department of Pediatric Surgery, Osaka Medical Center and Research Institute for Maternal and Child Health, Izumi, Osaka, Japan.

Journal of Pediatric Surgery
|December 11, 2003
PubMed

Insights

Pediatric congenital esophageal stenosis (CES) is linked to gastroesophageal reflux and abnormal esophageal motility. This study investigated esophageal function in children with CES, finding common motor and reflux issues.

Area of Science:

  • Pediatric Gastroenterology
  • Esophageal Motility Disorders
  • Congenital Anomalies

Background:

  • Congenital esophageal stenosis (CES) is a rare condition causing foregut symptoms in infants and children.
  • Understanding esophageal motor function in CES is crucial for diagnosis and management.

Purpose of the Study:

  • To investigate esophageal motor function in pediatric patients diagnosed with isolated congenital esophageal stenosis (CES).

Main Methods:

  • Study included four boys with CES (3 weeks to 4 years old) presenting with dysphagia or stridor.
  • Evaluations included esophagram, endoscopy, 24-hour esophageal pH monitoring, and manometry.
  • CES etiologies identified were fibromuscular stenosis (FMS), tracheobronchial remnants (TBR), and membranous diaphragm (MD).

Main Results:

  • Esophagram revealed contrast stasis proximal to distal esophageal narrowing in FMS/TBR cases.
  • No endoscopic esophagitis was observed.
  • Three patients showed pathologic esophageal acid exposure; manometry indicated synchronous contractions in FMS/TBR patients and peristaltic waves in the MD patient.
  • Incomplete lower esophageal sphincter (LES) relaxation occurred in FMS/TBR patients, though basal LES pressure was adequate.

Conclusions:

  • Gastroesophageal reflux is prevalent in pediatric patients with CES.
  • Impaired esophageal motility, including abnormal contractions and LES relaxation, is a common finding in CES.
Abstract

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