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A case of Omenn-like immunodeficiency syndrome
M Morren1, S Van Lierde, F Lacquet
1Department of Dermatology, University Hospital, Katholieke Universiteit Leuven, Belgium.
Dermatology (Basel, Switzerland)
|January 1, 1992
Abstract:
We report the case of a child with a variant of the Omenn immunodeficiency syndrome. He presented with erythroderma, lymphadenopathy, hepatosplenomegaly, failure to thrive, and recurrent purulent infections. The immunological studies showed marked disturbances in the subpopulations and functions of T lymphocytes, which suggests a defect in T cell differentiation as the cause of the disease.