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Intra-abdominal desmoplastic small cell tumour--a case report
Kaushik Debnath1, Thangjam Dhabali Singh, Laishram Pardesi Singh
1Department of Pathology, Regional Institute of Medical Sciences, Babina Diagnostic Centre and CCMC and Research Centre, Imphal, Manipur.
Indian Journal of Pathology & Microbiology
|March 18, 2004
Summary
A rare intra-abdominal desmoplastic small cell tumour (DSCT) was found in a 14-year-old boy. This uncommon childhood cancer presented without pain or ascites, showing transmural infiltration of the colon.
Area of Science:
- Pediatric Oncology
- Surgical Pathology
- Abdominal Neoplasms
Background:
- Desmoplastic small cell tumour (DSCT) is a rare, aggressive malignancy primarily affecting young males.
- Intra-abdominal presentation is common, often involving the peritoneum.
- Diagnosis can be challenging due to nonspecific symptoms.
Observation:
- A 14-year-old male presented with an intra-abdominal mass.
- The tumour originated from the transverse mesocolon.
- Notably, the patient lacked typical symptoms such as abdominal pain and ascites.
Findings:
- Histopathological examination confirmed desmoplastic small cell tumour.
- The tumour demonstrated transmural infiltration of the adjacent transverse colon.
- This case highlights an unusual presentation of a rare pediatric neoplasm.
Implications:
- This case expands the clinical spectrum of desmoplastic small cell tumour presentations.
- Early recognition of atypical presentations is crucial for timely diagnosis and treatment.
- Further research into the behavior and management of intra-abdominal DSCT is warranted.
