[Ehlers Danlos type IV syndrome presenting with simultaneous dissection of both internal carotid and both vertebral

K Mondon1, B de Toffol, G Georgesco

  • 1Service de Neurologie, CHRU de Tours, France. karl.mondon@wanadoo.fr

Revue Neurologique
|April 23, 2004
PubMed

Insights

Cervical artery dissection, a common cause of stroke in young adults, can be linked to connective tissue disorders. Ehlers-Danlos syndrome (EDS) is a key consideration for diagnosing and managing these dissections.

Area of Science:

  • Neurology
  • Vascular Surgery
  • Genetics

Background:

  • Cervical artery dissection is a significant cause of ischemic stroke in younger populations.
  • Prompt diagnosis and management are crucial for preventing neurological deficits.

Observation:

  • A 34-year-old patient presented with simultaneous dissection of both internal carotid and vertebral arteries.
  • The patient experienced recurrent right-sided motor deficits and persistent otalgia.

Findings:

  • Ehlers-Danlos syndrome type IV was diagnosed as the underlying etiology.
  • Connective tissue disorders, particularly vascular Ehlers-Danlos syndrome, should be investigated in cases of cervical artery dissection.

Implications:

  • Early identification of Ehlers-Danlos syndrome is vital for appropriate patient management.
  • Considering genetic connective tissue diseases can improve diagnostic yield in cervical artery dissection cases.
  • This case highlights the importance of a comprehensive etiological workup for cervical artery dissection.
Abstract

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