Congenital esophageal stenosis

Mahmoud A Machmouchi1, Mohamed Al Harbi, Khalid A Bakhsh

  • 1Department of Surgery, King Faisal Specialist Hospital and Research Centre, Jeddah, Kingdom of Saudi Arabia.

Insights

Congenital esophageal stenosis (CES) is a rare condition. Prompt diagnosis and treatment, including dilation or surgery, can effectively manage CES in infants, resolving swallowing issues and obstructions.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Medical Diagnostics

Background:

  • Congenital esophageal stenosis (CES) is a rare congenital anomaly affecting the esophagus.
  • CES typically presents in infancy but can be diagnosed later in life.
  • Early diagnosis is crucial for effective management and preventing complications.

Observation:

  • Two cases of CES in infants are presented.
  • Case 1: A one-month-old male infant with swallowing difficulties and recurrent pneumonias.
  • Case 2: An 18-month-old male infant with complete esophageal obstruction requiring a feeding gastrostomy.

Findings:

  • Diagnosis in Case 1 was confirmed via fluoroscopic esophagogram and endoscopy.
  • Simple esophageal dilatation successfully treated Case 1, resolving symptoms.
  • Case 2 required surgical intervention with resection and end-to-end anastomosis, with a successful outcome.

Implications:

  • CES can be effectively managed with timely and appropriate interventions.
  • Minimally invasive techniques like dilation may be sufficient for less severe cases.
  • Surgical options provide a viable solution for complete esophageal obstruction in CES.
  • These cases highlight the importance of recognizing CES in infants presenting with feeding and respiratory issues.

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