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Implantation of Total Artificial Heart in Congenital Heart Disease
Published on: July 18, 2014
Congenital coronary artery-left heart fistulas: Report of three cases
A Thomas Pezzella1, Giorgio Falaschi, David A. Ott
1Department of Cardiovascular Surgery of the Texas Heart Institute, Houston, Texas.
Insights
Surgical correction of congenital coronary artery fistulas terminating in the left heart is effective. Early elective ligation in childhood is recommended, even for asymptomatic patients, to prevent future complications.
Area of Science:
- Cardiovascular Surgery
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Congenital coronary artery fistulas are rare cardiac malformations.
- Fistulas terminating in the left heart present unique surgical challenges.
- Complications include rupture, endocarditis, and congestive heart failure, often age-related.
Purpose of the Study:
- To evaluate the surgical outcomes of congenital coronary artery fistulas terminating in the left heart.
- To emphasize the importance of timely surgical intervention.
- To support the recommendation for early elective ligation.
Main Methods:
- Review of 59 patients undergoing operative correction for congenital coronary artery fistulas.
- Focus on three cases with fistulas originating from a coronary artery and terminating in the left heart.
- Analysis of pre- and post-operative patient symptoms and complications.
Main Results:
- Three patients with left heart terminating fistulas underwent successful operative correction.
- All three symptomatic patients became asymptomatic after surgical repair.
- The findings support the efficacy of surgical intervention for these specific fistulas.
Conclusions:
- Operative correction of congenital coronary artery fistulas terminating in the left heart yields favorable outcomes.
- Early elective ligation during childhood is crucial, even in asymptomatic cases, to prevent age-related complications.
- Timely surgical management is essential for improving long-term prognosis in affected children.
Abstract:
Of 59 patients who underwent operative correction of congenital coronary artery fistulas from May 1956 through May 1980 at our institution, three had fistulas that arose from the coronary artery and terminated in the left heart. The chief indication for surgical correction in such patients is the presence of symptoms or the development of complications, which include rupture, endocarditis, and congestive heart failure. The principal objective of repair is closure or obliteration of the fistulous communication and preservation of distal myocardial perfusion. Because symptoms and complications tend to occur with age, elective ligation is warranted during childhood, even in asymptomatic patients. The three cases described here, as well as the reviewed series of left heart fistulas, substantiate this fact. All three patients were symptomatic before operation and asymptomatic afterward.
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