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Metabolic Pathway Confirmation and Discovery Through 13C-labeling of Proteinogenic Amino Acids
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Azelaic and pimelic acids: metabolic intermediates or artefacts?

M J Bennett1, M C Ragni, I Hood

  • 1Department of Pediatrics, Children's Hospital of Philadelphia.

Journal of Inherited Metabolic Disease
|January 1, 1992
PubMed
Summary

Elevated urinary azelaic and pimelic acids aid in diagnosing mitochondrial and peroxisomal beta-oxidation disorders. However, sample storage in plastic containers can cause artificial increases in these and other dicarboxylic acids.

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