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[Orbital meningoencephalocele: two case studies]
M Benharbit1, L Rifi L, A El Khamlichi
1Service d'Ophtalmologie A, Hôpital d'Oto-Neuro-Ophtalmolgie, Rabat, Maroc.
Journal Francais D'Ophtalmologie
|September 3, 2004
Summary
Primitive orbital meningoencephalocele, a rare congenital defect involving meninges and brain tissue herniation into the orbit, is effectively treated with a transcranial surgical approach for definitive recovery.
Area of Science:
- Neuroscience
- Developmental Biology
- Ophthalmology
Background:
- Primitive orbital meningocele is a rare congenital malformation characterized by meningeal herniation through orbital bone defects.
- Meningoencephalocele involves atrophic brain tissue within the herniated meningeal sac, differentiating it from simple meningocele.
Observation:
- Two infant cases presented with medial orbital tumoral syndrome.
- Computed tomography revealed cystic tumors near bony defects at the anterior frontoethmoidal junction.
Findings:
- A transcranial approach confirmed orbital meningoencephalocele.
- Surgical resection of the meningoencephalocele and closure of bony/dural defects resulted in an uneventful outcome.
Implications:
- Orbital meningoencephalocele is likely associated with abnormal rostral neuropore closure.
- Early diagnosis based on clinical and radiological features is crucial.
- Transnasal surgical treatment offers a definitive recovery for this condition.