Tracheal juvenile xanthogranuloma in a child

Juvenile xanthogranuloma is the most common form of non-Langerhans cell histiocytosis in children. It usually presents in the form of cutaneous lesions. Occasionally, the disease may affect other organs. Visceral forms are usually associated with cutaneous lesions, and are easily diagnosed. In isolated visceral occurrence, however diagnosis may prove difficult. Having the same spontaneous remission as cutaneous lesions, visceral lesions require treatment only in the case of serious dysfunction. We describe a case of isolated juvenile xanthogranuloma of the trachea, which has not previously been reported in children. The patient presented with serious respiratory symptoms that required immediate intervention.