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Lipofibromatosis presenting as a pediatric neck mass
B W Herrmann1, L P Dehner, J W Forsen
1Department of Otolaryngology-Head and Neck Surgery, Washington University School of Medicine, St. Louis Children's Hospital at Washington University Medical Center, St. Louis, MO, USA. bherrmann@childrensent.com
International Journal of Pediatric Otorhinolaryngology
|November 10, 2004
Summary
Lipofibromatosis, a rare pediatric soft tissue tumor, is characterized by adipose and fibroblast-like cells. This report details the first known case of lipofibromatosis occurring in a child's neck.
Area of Science:
- Pathology
- Pediatric Oncology
Background:
- Lipofibromatosis is a recently identified benign neoplasm in children.
- It is histologically distinct from other fibromatoses and lipoblastoma.
Observation:
- This benign tumor typically presents in the extremities.
- Key features include disorganized adipose lobules and spindled fibroblast-like cells.
Findings:
- This case represents the first documented instance of lipofibromatosis affecting the neck in a pediatric patient.
Implications:
- This finding expands the known anatomical distribution of lipofibromatosis.
- Highlights the importance of considering lipofibromatosis in pediatric neck masses.
