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Automated Sholl Analysis of Digitized Neuronal Morphology at Multiple Scales
Published on: November 14, 2010
[Shone's anomaly Fallbericht und Hintergrund]
Insights
Shone's anomaly, a rare congenital heart condition, can present in adults undergoing non-cardiac surgery. This case highlights the importance of recognizing this complex cardiac anomaly in adult surgical patients.
Area of Science:
- Cardiology
- Anesthesiology
- Medical Case Reports
Background:
- Shone's anomaly is a rare congenital heart condition characterized by four obstructive cardiac lesions.
- It is typically described in pediatric patients, with limited literature on adult perioperative presentations.
Observation:
- An adult patient with undiagnosed, incomplete Shone's anomaly presented for non-cardiac surgery.
- The anomaly included supravalvular mitral ring, mitral/subvalvular apparatus deformity, subvalvular aortic stenosis, and coarctation of the aorta.
Findings:
- The case report details the anesthetic management of this adult patient with unrecognized Shone's anomaly.
- It underscores the potential for incomplete forms of the anomaly to go undiagnosed into adulthood.
Implications:
- Highlights the need for heightened awareness of Shone's anomaly in adult patients undergoing non-cardiac surgery.
- Suggests that anesthesiologists should consider this rare condition in patients with complex cardiac histories or unexplained symptoms.
- Emphasizes the importance of thorough preoperative assessment for potentially undiagnosed congenital heart disease.
Abstract:
Shone's anomaly was first described in 1963 as a developmental complex of four potentially obstructive cardiac lesions including a supravalvular fibrous mitral ring, deformity of the mitral and/or subvalvular apparatus, subvalvular aortic stenosis and coarctation of the aorta. While paediatric patients with Shone's anomaly have been reported in the literature, only a few adult patients presenting with this anomaly have been described in the perioperative period. However, patients with an undiagnosed, incomplete form of Shone's anomaly might occasionally present for non-cardiac surgery as adults. In this case report we describe the anaesthetic management of an adult patient scheduled for a non-cardiac operation, who suffered from Shone's anomaly that was unrecognised prior to the operation.
