Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

Diffuse pulmonary lymphangiectasis with heart defect discovered 4 months post-natally.

J C Hoeffel1, F Marcon, A M Worms

  • 1Department of Radiology, Hôpital d'Enfants, Vandoeuvre, France.

Padiatrie Und Padologie
|January 1, 1992
PubMed
Summary

Congenital pulmonary lymphangiectasia, a rare and often fatal condition, can be survivable into childhood. This case report details an infant with this condition and congenital heart disease who lived to 11 years old.

Related Concept Videos

You might also read

Related Articles

Articles linked to this work by shared authors, journal, and citation graph.

Sort by
Same author

Advancing Genotoxicity Assessment by Building a Global AOP Network.

Environmental and molecular mutagenesis·2025
Same author

Evaluation of the clinical and economic impact of delays to surgery in patients with periampullary cancer.

BJS open·2019
Same author

Development and multicentre validation of a prognostic model to predict resectability of pancreatic head malignancy.

BJS open·2018
Same author

β-Alkylated oligomaltosides as new alternative preservatives: antimicrobial activity, cytotoxicity and preliminary investigation of their mechanism of action.

Journal of applied microbiology·2013
Same author

Impact of transesophageal electrophysiologic study to elucidate the mechanism of arrhythmia on children with supraventricular tachycardia and no preexcitation.

Pediatric cardiology·2013
Same author

[Transesophageal electrophysiological study in non sedated children younger than 11 years with a Wolff-Parkinson-White syndrome].

Annales de cardiologie et d'angeiologie·2008

Area of Science:

  • Pediatric Pulmonology
  • Cardiology
  • Medical Genetics

Background:

  • Congenital pulmonary lymphangiectasia (CPL) is a rare neonatal disorder characterized by lymphatic vessel dilation in the lungs.
  • It typically presents with respiratory distress at birth and has a high mortality rate.
  • Pulmonary interstitial syndrome is a common radiological finding in CPL.

Observation:

  • A case of an infant diagnosed with congenital pulmonary lymphangiectasia and co-existing congenital heart disease is presented.
  • The infant survived beyond the typical neonatal period, reaching 11 years of age.
  • This long-term survival challenges the generally accepted prognosis of CPL.

Findings:

  • The coexistence of congenital heart disease may influence the prognosis of congenital pulmonary lymphangiectasia.

Related Experiment Videos

  • This case highlights potential variations in the natural history of CPL.
  • Further research into pathogenic and nosologic aspects is warranted.

    • Implications:

    • This case suggests that long-term survival in CPL, especially with congenital heart disease, is possible.
    • It underscores the need for individualized prognostic assessments in rare pediatric lung diseases.
    • Understanding atypical presentations can improve management strategies for congenital pulmonary lymphangiectasia.