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Diffuse pulmonary lymphangiomatosis: imaging findings.
Ensar Yekeler1, Memduh Dursun, Abdurrahman Yildirim
1Departments of Radiology, Istanbul University Istanbul School of Medicine, Istanbul, Turkey.
Diagnostic and Interventional Radiology (Ankara, Turkey)
|March 30, 2005
Summary
Diffuse pulmonary lymphangiomatosis is a rare, progressive lymphatic disorder typically affecting young individuals. Imaging reveals characteristic lymphatic involvement in the chest, often leading to a fatal outcome.
Area of Science:
- Pulmonology
- Radiology
- Pathology
Background:
- Diffuse pulmonary lymphangiomatosis is a rare disorder of lymphatic channels.
- It primarily affects children and young adults, often with a fatal prognosis.
Observation:
- The disease involves lymphatic channels from the mediastinum to the pleura.
- Imaging shows mediastinal soft tissue infiltration and thickened pulmonary structures.
Findings:
- Spiral CT, high-resolution CT, and ultrasonography reveal characteristic findings in severe cases.
- The report details imaging manifestations of this rare pulmonary lymphatic disease.
Implications:
- Accurate imaging is crucial for diagnosing diffuse pulmonary lymphangiomatosis.
- Distinguishing it from similar lymphatic disorders is important for patient management.