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Complicated unroofed coronary sinus syndrome
Ghulam Sarwar1, Bilal Ahmed, Naeem Suleman
1Department of Cardiothoracic Surgery, The Aga Khan University Hospital, Karachi. sirvur01@yahoo.com
Summary
A rare congenital heart defect, unroofed coronary sinus, was unexpectedly discovered during surgery for atrial septal defect and mitral valve regurgitation. Successful surgical correction involved re-routing the left superior vena cava and valve replacement.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Surgical Innovation
Background:
- Planned surgical closure for atrial septal defect (ASD) and mitral valve regurgitation (MR) in a pediatric patient.
- Standard surgical approaches for complex congenital heart conditions.
Observation:
- Peroperative discovery of a complete unroofed coronary sinus (URCS), a rare anomaly.
- Co-existence of URCS with planned ASD and MR repair.
Findings:
- Successful intracardiac re-routing of the left superior vena cava (LSVC).
- Concomitant successful mitral valve replacement (MVR).
- Combined surgical correction of ASD, MR, URCS, and LSVC anomaly.
Implications:
- Highlights the importance of intraoperative echocardiography and vigilance for unexpected cardiac anomalies.
- Demonstrates the feasibility of complex, multi-stage intracardiac repairs in a single procedure.
- Improves understanding of surgical management strategies for combined congenital heart defects.