[A case of Bannayan-Zonana syndrome]

Bannayan Zonana syndrome is a very rare disease. The characteristic of this disease include macrocephaly, multiple benign tumors and various malformations. A 7-month-old baby with Bannayan-Zonana syndrome was scheduled for the repair of cleft lip and plate. The hight was 77 cm and weight was 9.8 kg, and he had macrocephaly with atrial septal defect and bilateral otitis media. No tumors had been detected in the airway by MRI before induction and the vocal cord could be visualized by laryngoscope. Anesthesia was induced with sevoflurane 5% and vecuronium 1 mg, and maintained with sevoflurane 1-2% and fentanyl 150 microg. At the end of the operation, nasal airways were inserted and we extubated in the operation room. He was discharged from ICU on the second postoperative day without complications.