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Subaortic obstruction and complete atrioventricular block in Behçet's disease
Philippe Unger1, Didier de Cannière, Nicolas Preumont
1Department of Cardiology, Erasme Hospital, Université Libre de Bruxelles, 808 route de Lennik, B-1070 Brussels, Belgium. punger@ulb.ac.be
Summary
Behçet's disease can cause rare left ventricular outflow tract obstruction due to interventricular septal pseudo-aneurysms. This case highlights a unique presentation of subaortic stenosis and atrioventricular block.
Area of Science:
- Cardiology
- Internal Medicine
- Rheumatology
Background:
- Left ventricular outflow tract (LVOT) obstruction is typically dynamic, often linked to hypertrophic cardiomyopathy or congenital anomalies like subaortic stenosis.
- Behçet's disease is a multisystem inflammatory disorder with rare cardiovascular manifestations.
Observation:
- A patient presented with a systolic murmur, fever, and syncope, indicative of potential cardiac compromise.
- Diagnostic workup revealed a rare cause of subaortic obstruction.
Findings:
- The obstruction was attributed to a pseudo-aneurysm dissecting the interventricular septum.
- The patient also exhibited a complete atrioventricular block, complicating the cardiac presentation.
Implications:
- This case expands the spectrum of cardiovascular complications associated with Behçet's disease.
- It underscores the importance of considering rare etiologies for LVOT obstruction and atrioventricular block in patients with systemic inflammatory conditions.