Related Experiment Video
Updated: Jun 10, 2026
09:33
Genetic Profiling and Genome-Scale Dropout Screening to Identify Therapeutic Targets in Mouse Models of Malignant Peripheral Nerve Sheath Tumor
Published on: August 25, 2023
Peripheral primitive neuroectodermal tumour of the maxilla.
Guowen Sun1, Zubing Li, Jinrong Li
1Department of Oral and Maxillofacial Surgery, College and Hospital of Stomatology, Wuhan University, 237 Luoyu Road, Wuhan 430079, PR China. guowensun@hotmail.com
The British Journal of Oral & Maxillofacial Surgery
|October 6, 2005
Summary
Peripheral primitive neuroectodermal tumors (pPNET) are rare, aggressive soft tissue neoplasms typically affecting younger individuals. This report details an unusual case of pPNET occurring in the maxilla of a 49-year-old woman.
Area of Science:
- Oncology
- Pathology
- Medical Imaging
Background:
- Peripheral primitive neuroectodermal tumors (pPNET) are rare, highly malignant neoplasms.
- These tumors predominantly affect children and young adults.
- Maxillary PNET is an exceptionally rare presentation.
Observation:
- A 49-year-old woman presented with a pPNET of the maxilla.
- Clinical and radiological findings were evaluated.
- Histopathological examination confirmed the diagnosis.
Findings:
- The case highlights an atypical age and location for pPNET.
- Diagnostic challenges in rare soft tissue neoplasms are noted.
- Successful management strategies for maxillary PNET were explored.
Implications:
- This case expands the known clinical spectrum of pPNET.
- It underscores the importance of considering rare diagnoses in soft tissue tumors.
- Further research into the etiology and treatment of adult maxillary pPNET is warranted.
