Association of a sylvian arachnoid cyst and trigonocephaly in a developing child: importance and management

Alp Ozgün Börcek1, Hakan Emmez, Fikret Doğulu

  • 1Department of Neurosurgery, Gazi University, Ankara, Turkey. alpob@yahoo.com

Insights

Trigonocephaly and sylvian arachnoid cysts are rare co-occurrences that can increase intracranial pressure. This case demonstrates successful simultaneous surgical correction of both conditions in an infant.

Area of Science:

  • Neurosurgery
  • Pediatric Neurosurgery
  • Craniofacial Surgery

Background:

  • Trigonocephaly (metopic synostosis) and arachnoid cysts can independently cause increased intracranial pressure.
  • The combined incidence of trigonocephaly and sylvian arachnoid cysts is not well-documented.
  • This report addresses a rare case of this dual pathology.

Observation:

  • An 11-month-old girl presented with trigonocephaly (triangular forehead) and a Type II sylvian arachnoid cyst.
  • Neurological examination was normal, with no history of seizures or other systemic malformations.
  • The patient had metopic suture synostosis.

Findings:

  • Surgical intervention involved simultaneous forehead reconstruction (advancement) for trigonocephaly and fenestration of the sylvian arachnoid cyst.
  • The arachnoid cyst was fenestrated into the basal cisterns.
  • A satisfactory surgical outcome was achieved.

Implications:

  • The coexistence of craniosynostosis and arachnoid cysts is uncommon.
  • Simultaneous surgical management of trigonocephaly and associated sylvian arachnoid cysts is feasible and effective.
  • This approach offers a single-session treatment option for complex pediatric neurosurgical cases.
Abstract