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Giant terminal lipomyelocystocele
Deepak Kumar Gupta1, Shashank Ramdurg, A K Mahapatra
1Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India. drdeepakkumargupta@yahoo.com
Pediatric Neurosurgery
|December 17, 2005
Summary
A rare spinal condition, terminal lipomyelocystocele, involves herniation of the spinal cord through spina bifida. Early surgical intervention is crucial for managing this congenital anomaly.
Area of Science:
- Pediatric Surgery
- Neuroscience
- Developmental Biology
Background:
- Terminal myelocystocele is a rare congenital condition characterized by the herniation of the hydromyelic caudal spinal cord and subarachnoid space through a posterior spina bifida.
- It is a form of occult spinal dysraphism, often presenting with significant neurological deficits.
Observation:
- A 1-year-old female infant presented with a large lumbosacral mass, flaccid paraplegia, and lifelong urinary incontinence.
- Imaging revealed a low-lying conus with a conus lipoma, a dilated central canal, and a meningocele, consistent with terminal lipomyelocystocele.
Findings:
- The patient had a giant terminal lipomyelocystocele, measuring 30 x 20 x 10 cm, which is exceptionally large and unprecedented in medical literature.
- Surgical correction of the giant terminal lipomyelocystocele was successfully performed.
Implications:
- Terminal myelocystocele should be considered in the differential diagnosis of congenital lumbosacral masses.
- Early surgical management is recommended to improve outcomes for patients with this condition.
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