Atypical chondroid syringoma

In summary, chondroid syringoma is a rare sweat gland neoplasm characterized by its slow growth and unpredictable growth phase. When malignant, it has a significant potential for recurrence, metastases, and even death. Due to the rarity of this tumor, an accurate preoperative diagnosis is difficult. Therefore, it is important for the clinician to have a high degree of suspicion for chondroid syringoma when considering the differential diagnosis of solid cutaneous nodules. A patient has been presented with a chondroid syringoma with atypical features, but no unequivocal evidence of malignancy. This poses a therapeutic dilemma. At the present time, the best therapeutic option appears to be accurate diagnosis, wide local excision, and close follow-up. Further research will elucidate the role of adjunctive treatment modalities.